Epidermolysis bullosa simplex is one of a group of genetic conditions called epidermolysis bullosa that cause the skin to be very fragile and to blister easily. Epidermolysis bullosa (EB) is a group of genetic conditions that result in easy blistering of the skin and mucous membranes. Blisters occur with minor trauma or . Prevención de Ampollas. Como cargar al bebé: Evite levantar el bebé o niño por debajo de los brazos. En su lugar, ponga una mano debajo del trasero y la otra.

Author: Maulabar Gardagal
Country: Iceland
Language: English (Spanish)
Genre: Science
Published (Last): 4 December 2011
Pages: 420
PDF File Size: 17.33 Mb
ePub File Size: 2.29 Mb
ISBN: 167-5-60848-496-1
Downloads: 60435
Price: Free* [*Free Regsitration Required]
Uploader: Grokasa

Two case reports with year follow-up. Agujas esterilizadas o lancetas pueden ser usadas para perforar la orilla del techo de la ampolla. Accessed June 19, Views Read Edit View history. British Journal of Dermatology. All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.

Clinical management for epidermolysis bullosa dystrophica

Infobox medical condition new Articles needing additional medical references from October All articles needing additional references Articles requiring reliable medical sources All articles with unsourced statements Articles with unsourced statements from March Articles with unsourced statements from April Commons category link from Wikidata RTT.

Retrieved 21 December Specific genetic mutations are well characterized for most the different EB subtypes and variants. The presentation and severity of EB are affected by the specific genetic defects causing the disease, and can be difficult to classify. Combined medical-dental treatment of an epidermolysis bullosa patient. The human skin consists of two layers: Genetic counseling Transmission is autosomal dominant and sporadic cases are frequent.


It may be inherited in a recessive or dominant manner.

The major dental complication of EB in general is the increased risk of caries 3. The patient reported feeding difficulties only when the blisters were very painful. Contact your doctor if you or your child develops blisters, epidermoliis if you don’t know the reason for them. Fluoridated varnish was applied on white spot lesions.

Types of Epidermolysis Bullosa

Epideemolisis disease gene may be passed on from one parent who has the disease autosomal dominant inheritance. Request an Appointment at Mayo Clinic. Epidermolysis bullosa simplex Epidermolysis bullosa simplex usually becomes apparent at birth or during early infancy.

Oral-clinical findings and management of epidermolysis bullosa. Dental treatment for patients with EB consists of palliative therapy for its oral manifestations along with typical restorative and periodontal procedures.

EBA is a non-genetic autoimmune diseasecaused by the development of antibodies proteins that attack foreign substances against type VII collagen, an essential skin protein.

Dental plaque was controlled with professional prophylaxis and use of 0. In the most severe cases, scars may cause either ankyloglossia or microglossia 3, Her fingernails and toenails were absent and epidermolieis hands showed some degree of deformity.


In both cases presented in this work, blisters formed after mild pressure on the mouth 15,16 and during administration of local anesthetic solution 11 Case 1.

Epidermolysis bullosa

Uso prolongado de Bactroban ha sido asociado con el desarrollo de infecciones de Estafilococo Resistente. Given the considerable overlap between non-Dowling-Meara EBS and localized EBS within some kindreds, some experts prefer to group both subtypes together.

It also presents with blisters at the site of friction, especially on the hands and feet, and has variants that can occur in children and adults. What is Epidermolysis Bullosa EB? Journal of Dermatological Treatment.

After six days of treatment with G-CSF, the size of the open lesions were reduced by a median of Localized epidermolysis bullosa simplex with generalized enamel hypoplasia in a child. Epidermolysis Bullosa ep-i-der-mo-lie-sis bu-low-suhor EB, is a rare genetic connective tissue disorder that affects 1 out of every 20, births in the United States approximately children a year are born with EB.

Bullous pemphigoidpemphigus vulgarisfriction blisters, epidermolisia bites [4]. Or it may be passed on from both parents autosomal recessive inheritance or arise as a new mutation in the affected person that can be passed on.